Miroslav Šašinka1, Katarína Furková1, Dušan Daniš2
Kidney are often connected with various cysts what are important primary cause of the chronic kidney disease. For their importance witness cystic kidney findings till 10 % of patients with terminal renal failure. Mostly they are hereditary polycystic kidney diseases and paediatricians until now devoted attention namely to autosomal recessive polycystic kidney disease. However, often also first symptoms of the autosomal dominant polycystic kidney disease began in infancy and in last time funded good effects of the long acting somatostatin analogue – octreotid and specially tolvaptan, which can very probably reverse bad prognosis of this disease, if therapy begins early. New facts need increase paediatricians knowledge’s about autosomal dominant polycystic kidney disease. Authors analyse genetics, pathophysiology, diagnostics and prognosis of this disease with specially intension on new therapeutic methods.