Miloš Mlynček, Peter Uharček, Dušan Ďurčanský
Langerhans cell histiocytosis is a rare proliferative disorder of Langerhans cells with uncertain aetiology, wide spectrum of clinical symptoms and varied behaviour. The authors describe an additional case of LCH in which the disease was confined to the vulva and was treated with radical vulvectomy. The difficulty of the treatment also lies in the unpredictability of the course of LCH. Further research needs to be conducted so that we can better understand the aetiology, pathogenesis and rational management of this disorder.